Degenerative leiomyopathy
WebJun 1, 2015 · Degenerative leiomyopathy. The condition is also known as hollow visceral myopathy. There is progressive loss of intestinal smooth muscle with associated fibrosis. The urinary bladder is also usually affected but other extra-intestinal manifestations are unusual – a point of distinction from systemic myopathies. The disease is usually patchy ... WebJul 21, 2016 · Degenerative Myelopathy. July 21, 2016. Degenerative myelopathy is a degenerative disease of the spinal cord that begins in older adulthood and progresses …
Degenerative leiomyopathy
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WebDegenerative leiomyopathy (DL) is a distinctive form of acquired degenerative visceral myopathy of uncertain etiology that occurs largely in Africa and results in … WebFeb 25, 2006 · The syndrome of degenerative leiomyopathy causing intestinal obstruction clinically manifests in young indigenous African children as massive megacolon without aganglionosis. Eighteen children...
WebDegenerative leiomyopathy (DL) is a distinctive form of acquired degenerative visceral myopathy of uncertain aetiology. It occurs mainly in Africa and results in intestinal pseudo-obstruction (IP WebDec 20, 2024 · Abstract. Visceral myopathy is a rare bowel disease affecting peristalsis and causing pseudo-obstruction. There is no specific treatment for chronic intestinal pseudo-obstruction caused by visceral myopathy. We report a case of a 30-year-old woman with visceral myopathy who, due to unsuccessful conservative treatment, underwent surgery.
WebNov 16, 2024 · Degenerative leiomyopathy is a distinctive entity with classical clinical and histological features. The aetiology is still obscure. View. Show abstract. Recommended publications. WebMar 8, 2024 · Degenerative leiomyopathy can also be secondary to anthracycline-based chemotherapeutic drugs. Histologically, the muscularis propria shows features of generation and replacement by fibrosis ( Fig. 11.15). The ganglion cells and the ganglia are however normally seen . Management of this rare disease remains supportive including …
WebFrontal Grossly dilated large bowel loops. Dilated bowel with fecal material, predominantly on the right. A kidney/coffee bean sign with a thick inner wall of opposed …
WebFeb 1, 1992 · Muscular disorders include degenerative leiomyopathy and mitochondrial disorders. The nervous or muscular system may also be affected secondarily in many systemic disorders. Surgical intervention is frequent in cases of chronic intestinal pseudo-obstruction and yields specimens for pathological examination. The pathological … summit healthplex ptWebDegenerative leiomyopathy • Indigenous to young children from southern, central and eastern Africa • not inherited • primarily affects the distal bowel • may affect the urinary tract • long history of increasing abdominal distention • progressive clinical deterioration • aetiology remains unknown summit health pediatrics westfield njWebFeb 22, 2013 · Background . Visceral myopathy is rare pathological condition of gastrointestinal tract with uncertain clinical presentation and unknown etiology. It often presents with symptoms of chronic intestinal pseudoobstruction of colon. We report a case of visceral myopathy which presented to us as acute appendicitis and Ogilvie … summit health portal chambersburg paWebDegenerative leiomyopathy (DL) is a distinctive form of acquired degenerative visceral myopathy of uncertain etiology that occurs largely in Africa and results in intestinal … summit health plan oregonWebSummary. African degenerative visceral leiomyopathy (ADL) is a distinctive visceral myopathy with onset in childhood. It presents as intestinal pseudoobstruction with a … summit healthplex fax numberWeb@article{Kaschula1987DegenerativeLW, title={Degenerative leiomyopathy with massive megacolon. Myopathic form of chronic idiopathic intestinal pseudo-obstruction occurring in indigenous Africans.}, author={Ronald Otto Christian Kaschula and Sidney Cywes and A Katz and Jan Hendrick Louw}, journal={Perspectives in pediatric pathology}, year={1987 ... pale yellow discharge from woundWebDec 11, 2024 · African degenerative leiomyopathy (ADL, DL, Bantu pseudo-Hirschsprung's disease) is a distinctive visceral myopathy, of unknown etiology, occurring in Africa. It has a classical clinical and histologic picture in young indigenous African children. It presents as intestinal pseudo-obstruction with a massive megacolon due to degeneration … summit healthplex mammogram